Aim of this publication is to offer readers a comprehensive surgical textbook that addresses exclusively rare liver and biliary diseases in pediatric and adult populations. It will  explain the origin of these types of diseases and provide guidance about their clinical manifestation, diagnosis, and treatment options. State-of-the-art research in the areas will be presented. Written by a multidisciplinary team of world-renowned experts, this textbook addresses the knowledge gap surrounding these rare diseases. Many medical professionals—specialists as well as general practitioners—are unfamiliar with these conditions due to their rarity. This book is designed for medical clinicians, including medical students and residents, PhD candidates, and postdoctoral researchers. Multiple specialties, such as oncology, surgery, pediatrics, and endocrinology, will find this book an invaluable reference.